An Atypical and Severe Case of Neuralgic Amyotrophy

Authors

  • Rui Cadilha Department of Physical and Rehabilitation Medicine, Centro Hospitalar São João, Porto
  • Hugo Amorim Department of Physical and Rehabilitation Medicine, Centro Hospitalar São João, Porto
  • Madalena Pinto Department of Physical and Rehabilitation Medicine, Centro Hospitalar São João, Porto
  • Fernando Silveira Department of Physical and Rehabilitation Medicine, Centro Hospitalar São João, Porto
  • Fernando Parada Department of Physical and Rehabilitation Medicine, Centro Hospitalar São João, Porto

DOI:

https://doi.org/10.25759/spmfr.267

Keywords:

Brachial Plexus Neuritis, Shoulder Pain

Abstract

Neuralgic amyotrophy or Parsonage-Turner syndrome is an uncommon disorder, of unknown etiology, typically characterized by abrupt onset of shoulder and upper extremity pain followed by progressive neurologic deficits. An immune/autoimmune process seems to have more support in development of neuralgic amyotrophy. Neuralgic amyotrophy is a clinical diagnosis, however, further diagnostic studies can confirm clinical suspicion and help exclude other causes. The treatment consists predominantly in pain control and rehabilitation. Patients with neuralgic amyotrophy, can be evaluated by a wide range of clinical specialists in the early stage of disease before a correct diagnosis be made. This is a result of different phenotypes that this disorder exhibits, that complicate the diagnosis. It is important for clinicians to beware of the classic clinical manifestations that usually follow a characteristic clinical course of abrupt onset of shoulder girdle pain followed by progressive neurologic deficits as muscle weakness, amyotrophy and sensory abnormalities. We report the case of a 32-year-old man who had a severe bilateral and atypical shoulder involvement, that made the most probably diagnostic not so evident.

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References

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How to Cite

1.
Cadilha R, Amorim H, Pinto M, Silveira F, Parada F. An Atypical and Severe Case of Neuralgic Amyotrophy. SPMFR [Internet]. 2017 Dec. 23 [cited 2025 Feb. 23];29(2):36-40. Available from: https://spmfrjournal.org/index.php/spmfr/article/view/267

Issue

Section

Case Report

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